From: Phenotypes and outcome of diffuse pulmonary non-amyloid light chain deposition disease
Hazard Ratio | 95% CI | p | |
---|---|---|---|
Demographic data | |||
Age at onset of symptoms, mean | 0.945 | 0.904—0.988 | 0.013 |
Age at diagnosis, mean | 0.942 | 0.902—0.983 | 0.0057 |
Sex | 0.714 | 0.435—1.169 | 0.18 |
Smoking status | 0.955 | 0.352—2.587 | 0.93 |
Lung function parameters | |||
FEV1, % pred | 0.974 | 0.955—0.994 | 0.012 |
FVC, % pred | 0.985 | 0.962 -1.01 | 0.21 |
FEV1/FVC, % | 0.942 | 0.903—0.982 | 0.005 |
TLC, % pred | 1.023 | 0.989—0.982 | 0.19 |
DLCO, % pred | 0.971 | 0.942—1.002 | 0.06 |
KCO, % pred | 0.980 | 0.945—1.015 | 0.26 |
6-min walk test, m | 0.995 | 0.987 – 1.003 | 0.21 |
Mean ∆FEV1, ml/year | 1.007 | 1.003 – 1.011 | 0.00095 |
Mean ∆DLCO, %/year | 1.039 | 0.827 – 1.305 | 0.75 |
Serum light chains | |||
Mean kappa light chain in serum, mg/L | 1.001 | 0.999 – 1.002 | 0.30 |
Mean lambda light chain in serum, mg/L | 1.016 | 0.898 – 1.150 | 0.80 |
Mean serum kappa/lambda ratio | 1.008 | 0.997 – 1.019 | 0.14 |
Predominant pattern (cystic/bronchiectasis) | 0.491 | 0.226 – 1.069 | 0.07 |